Juvenile Temporal Arteritis Clinically Masquerading as Temporal Artery Pseudoaneurysm

Alan S. Marcus, MD, Billie S. Fyfe, MD


Juvenile temporal arteritis (JTA) is a rare and controversial diagnosis. The clinical features include: age younger than 40 years old, temporal nodule with or without pain, no systemic features and no recurrences or systemic symptoms upon follow up.  The histopathologic features include intimal hyperplasia, endothelial hyperplasia, disruption of the internal elastic lamina and a lymphoeosinophilic panarteritis that lacks germinal centers and granulomatous inflammation.  The differential diagnosis consists of angiolymphoid hyperplasia with eosinophilia (ALHE) and Kimura disease.  It is debated whether JTA is a distinct diagnosis or a subset of ALHE or Kimura disease. We report a case of an 18-year-old man with a clinical presentation of temporal artery psuedoaneurysm, but with histopathologic features of JTA.  The patient has not sought further treatment 2.5 years after the original excision. 

[N A J Med Sci. 2013;6(2):95-99.   DOI:  10.7156/najms.2013.0602095]


juvenile temporal arteritis, angiolymphoid hyperplasia with eosinophilia, Kimura disease, temporal artery, temporal artery pseudoaneurysm

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